Congenital Desmoid Fibroma of the Soft Tissues in a 6-Month-Old Girl

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Published: 2024-01-15

Page: 1-5


Karima Atarraf *

Department of Pediatric Traumato-Orthopedics, Faculty of Medicine and Pharmacy, University of Mohamed Ben Abdellah, Fez, Morocco.

Fatoumata Binta Baldé

Department of Pediatric Traumato-Orthopedics, Faculty of Medicine and Pharmacy, University of Mohamed Ben Abdellah, Fez, Morocco.

Ayoub Boutahar

Department of Pediatric Traumato-Orthopedics, Faculty of Medicine and Pharmacy, University of Mohamed Ben Abdellah, Fez, Morocco.

Mohamed Tazi Charki

Department of Pediatric Traumato-Orthopedics, Faculty of Medicine and Pharmacy, University of Mohamed Ben Abdellah, Fez, Morocco.

Hicham Abdellaoui

Department of Pediatric Traumato-Orthopedics, Faculty of Medicine and Pharmacy, University of Mohamed Ben Abdellah, Fez, Morocco.

My Abderrahmane Afifi

Department of Pediatric Traumato-Orthopedics, Faculty of Medicine and Pharmacy, University of Mohamed Ben Abdellah, Fez, Morocco.

*Author to whom correspondence should be addressed.


Abstract

A desmoid tumor (DT), also known as aggressive fibromatosis, is a benign neoplasia of the soft tissues. It arises from conjonctive tissues, fascial sheaths, and muscular aponeurotic structures of muscles. According to biological characteristics, they are classified into three groups: -sporadic, -associated with familial adenomatous polyposis, -and familial or multicentric form. The pediatric form is ranged as a fourth group. To our knowledge, we report the first case in the world of congenital desmoid fibroma in the soft tissues of the ankle in a 6-month-old girl who is treated by surgical resection, with a good evolution over a 6-year follow-up. Through this observation, the authors suggest a review of the literature.

Keywords: Desmoid fibroma, newborn, female


How to Cite

Atarraf , K., Baldé , F. B., Boutahar, A., Charki , M. T., Abdellaoui , H., & Afifi , M. A. (2024). Congenital Desmoid Fibroma of the Soft Tissues in a 6-Month-Old Girl. Asian Journal of Medical Case Reports, 6(1), 1–5. Retrieved from https://globalpresshub.com/index.php/AJMCR/article/view/1979

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